Gasoyan H et al
Orange: water, Lcarnitine, acidity regulators citric acid and malic acid, orange emulsion (aroma, colouring agents E-104 and E-110 - may have an adverse effect on activity and attention in children), preservative potassium sorbate, calcium D-pantothenate (vitamin B5), preservative sodium benzoate, sweeteners acesulfame K and sucralose, pyridoxine hydrochloride (vitamin B6), sweetener steviol glycosides
At week 5, the dosage is typically raised to 5 mg once a week for another 4 weeks
Evidence-based titration schedules and Canadian sourcing in 2026
L.OshimaM.AgarwalR.ArnottC.CherneyD
Continuous venovenous haemodialysis (CVVHD) and continuous peritoneal dialysis (CPD) in the acute management of 21 children with inborn errors of metabolism